pyruvate dehydrogenase - definitie. Wat is pyruvate dehydrogenase
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Wat (wie) is pyruvate dehydrogenase - definitie


Pyruvate dehydrogenase kinase         
  •  doi = 10.1016/0006-291X(74)90461-6 }}</ref>
CLASS OF ENZYMES
(pyruvate dehydrogenase (acetyl-transferring)) kinase; EC 2.7.1.99; EC 2.7.11.2; PDHK; STK1; ATP:(pyruvate dehydrogenase (acetyl-transferring)) phosphotransferase
Pyruvate dehydrogenase kinase (also pyruvate dehydrogenase complex kinase, PDC kinase, or PDK; ) is a kinase enzyme which acts to inactivate the enzyme pyruvate dehydrogenase by phosphorylating it using ATP.
Pyruvate dehydrogenase deficiency         
  • Citric acid cycle with aconitate 2
  • Glycolysis
  • Microcephaly and a normal head size
  • MRI of head(brain)- cerebral atrophy can be detected by such a method<ref name=emed/>
CARBOHYDRATE METABOLIC DISORDER CHARACTERIZED BY THE BUILDUP OF LACTIC ACID IN THE BODY AND A VARIETY OF NEUROLOGICAL PROBLEMS AND CAUSED BY A DEFICIENCY OF ONE OF THE THREE ENZYMES IN THE PYRUVATE DEHYDROGENASE COMPLEX
Pyruvate dehydrogenase complex deficiency disease; Deficiency of pyruvate dehydrogenase
Pyruvate dehydrogenase deficiency (also known as pyruvate dehydrogenase complex deficiency or PDCD) is a rare neurodegenerative disorders associated with abnormal mitochondrial metabolism. PDCD is a genetic disease resulting from mutations in one of the components of the pyruvate dehydrogenase complex (PDC).
(pyruvate dehydrogenase (acetyl-transferring))-phosphatase         
CLASS OF ENZYMES
EC 3.1.3.43; (pyruvate dehydrogenase (acetyl-transferring))-phosphate phosphohydrolase
In enzymology, a [pyruvate dehydrogenase (acetyl-transferring)]-phosphatase () is an enzyme that catalyzes the chemical reaction